Desmoplastic small round cell tumor: A case report of a rare differential diagnosis of solid tumors of the pleura

Cao,Yuan; Chen,Ying; Yang,Li; Qian,Zi‑Hua; Han,Shu‑Gao; Li,Qing‑Hai; Yu,Ri‑Sheng

doi:10.3892/ol.2015.3680

Desmoplastic small round cell tumor: A case report of a rare differential diagnosis of solid tumors of the pleura

Authors:
- Yuan Cao
- Ying Chen
- Li Yang
- Zi‑Hua Qian
- Shu‑Gao Han
- Qing‑Hai Li
- Ri‑Sheng Yu
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Affiliations: Department of Pathology, The Second Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou, Zhejiang 310009, P.R. China, Department of Radiology, The Second Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou, Zhejiang 310009, P.R. China
Published online on: September 7, 2015 https://doi.org/10.3892/ol.2015.3680
Pages: 2991-2995

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Abstract

Desmoplastic small round cell tumor (DSRCT) presents as a rare separate clinical pathological entity, and pleural DSRCT is very rare. Following review of the English literatures it was revealed that, to date, <15 cases of primary DSRCT of the pleura have been reported worldwide. Among these, there are few computed tomography (CT) findings of pleural DSRCT which have previously been described in detail. The present study reports a pathologically proven case of pleural DSRCT, with varying contrast CT findings in a 72‑year‑old female, which appeared as a large (12.0x10.0x6.5 cm), smooth, oval mass in the left lower thorax with slight‑moderate uniform enhancement on contrast‑enhanced CT. To the best of our knowledge, the present report is the first to describe the large solid‑tumor pattern and the patient is the eldest reported case of pleural DSRCT.

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