Hepatic multiple perivascular epithelioid cell neoplasm: A case report and literature review

Lan,Yin  Zhi; Hua,Xiao  En

doi:10.3892/mco.2016.735

Hepatic multiple perivascular epithelioid cell neoplasm: A case report and literature review

Authors:
- Yin Zhi Lan
- Xiao En Hua
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Affiliations: The Second Xiangya Hospital of Central South University, Changsha, Hunan 410011, P.R. China
Published online on: January 22, 2016 https://doi.org/10.3892/mco.2016.735
Pages: 619-621

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Abstract

Perivascular epithelioid cell neoplasm (PEComa) is a rare tumor type and primary hepatic multiple perivascular is rarer still. The present case report investigated the case of a 40‑year‑old woman who was admitted to The Second Xiangya Hospital for hepatic multiple tumor by physical examination without any history of abdominal pain or body weight loss. Abdominal plain computed tomography revealed three lesions in the liver. All lesions exhibited a well‑defined boarder and only one mass contained fatty tissue in S6 of the liver. An enhanced scan revealed that all lesions were heterogeneous, and were enhanced on the artery phase and on portal vein phase. On delay phase, the lesions revealed continued enhancement, which is isoattenuating to the normal hepatic parenchyma. Following excision of the three masses, the patient was pathologically diagnosed with hepatic multiple PEComa. Short-term re-examination revealed no recurrence.

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