Primary desmoplastic small round cell tumor of the testis: A case report and review of the literature

He,Lang; Wen,Shimin; Hu,Xin; Guo,Cuihua; Yi,Cheng

doi:10.3892/ol.2013.1421

Primary desmoplastic small round cell tumor of the testis: A case report and review of the literature

Authors:
- Lang He
- Shimin Wen
- Xin Hu
- Cuihua Guo
- Cheng Yi
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Affiliations: Department of Abdominal Cancer, Cancer Center of West China Hospital, West China Medical School, Sichuan University, Chengdu, Sichuan 610041, P.R. China, Cancer Center, The Second Affiliated Clinical Medicine School of North Sichuan Medical College, Nanchong Central Hospital, Nanchong, Sichuan 637000, P.R. China
Published online on: June 25, 2013 https://doi.org/10.3892/ol.2013.1421
Pages: 565-567

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Abstract

Desmoplastic small round cell tumors (DSRCTs) are extremely rare and mainly affect adolescents and young adults. The tumors are usually involved with the abdominal area and/or the pelvic peritoneum. Only a small number of cases have been reported concerning DSRCTs of the testicular region. The present study reports a case of DSRCT of the testis with radical orchectomy and systemic chemotherapy, leaving the patient disease-free for 14 months. However, the patient died of multiple metastasis 12 months later. Furthermore there is a review of the English literature to analyze the incidence, site of origin, imaging and pathological characteristics of DSRCT.

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