Primary retroperitoneal perivascular epithelioid cell neoplasm: A case report

Liang,Wenjie; Xu,Chang; Chen,Feng

doi:10.3892/ol.2015.3210

Primary retroperitoneal perivascular epithelioid cell neoplasm: A case report

Authors:
- Wenjie Liang
- Chang Xu
- Feng Chen
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Affiliations: Department of Radiology, The First Affiliated Hospital, College of Medicine, Zhejiang University, Hangzhou, Zhejiang 310003, P.R. China, Department of Radiology, Hospital Affiliated to Binzhou Medical University, Binzhou, Shandong 256603, P.R. China
Published online on: May 14, 2015 https://doi.org/10.3892/ol.2015.3210
Pages: 469-472

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Abstract

Perivascular epithelioid cell neoplasm (PEComa) is a rare type of tumor, and primary retroperitoneal PEComa is rarer still. The present report discusses the case of a 51-year-old woman who was admitted to hospital following stiffness and discomfort in the upper right abdomen for longer than one month. Computed tomography identified a soft tissue mass in the rear right kidney, accompanied by clear cystic degeneration and bleeding. The borderline between the mass and the right kidney was not distinct. An enhanced scan revealed that the solid section of the mass was progressively enhanced. Following excision of the mass and the affected right kidney, the patient was pathologically diagnosed with retroperitoneal PEComa involving the right kidney. Short-term reexamination did not detect any recurrence.

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