Epithelioid angiomyolipoma mimicking adrenal cortical carcinoma: A diagnostic pitfall

Komarowska,Hanna; Bednarek‑Rajewska,Katarzyna; Kański,Marcin; Janicka‑Jedyńska,Małgorzata; Gut,Paweł; Ruchała,Marek

doi:10.3892/ol.2015.3543

Epithelioid angiomyolipoma mimicking adrenal cortical carcinoma: A diagnostic pitfall

Authors:
- Hanna Komarowska
- Katarzyna Bednarek‑Rajewska
- Marcin Kański
- Małgorzata Janicka‑Jedyńska
- Paweł Gut
- Marek Ruchała
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Affiliations: Department of Endocrinology, Metabolism and Internal Medicine, Poznań University of Medical Sciences, Poznań 60‑355, Poland, Department of Clinical Pathomorphology, Poznań University of Medical Sciences, Poznań 60‑355, Poland, Department of Geriatric Medicine and Gerontology, Poznań University of Medical Sciences, Poznań 60‑355, Poland
Published online on: July 29, 2015 https://doi.org/10.3892/ol.2015.3543
Pages: 2130-2134
Copyright: © Komarowska et al. This is an open access article distributed under the terms of Creative Commons Attribution License.

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Abstract

Epithelioid angiomyolipoma (EAML) is a rare mesenchymal neoplasmic variant of angiomyolipoma characterized by aggressive growth and unpredictable outcome. Cases of local recurrence and distant metastasis have been described. The histopathological diagnosis may be difficult, as EAML often mimics other neoplasms. This is the case report of a 39‑year‑old male patient with EAML, which was initially diagnosed as adrenal cortical carcinoma, due to the lack of cooperation between clinicians and pathologists.

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